Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) syndrome is a rare congenital coronary artery anomaly.
There are two types of ALCAPA syndrome: the infant type and the adult type, each of which has different manifestations and outcomes.
Infants experience myocardial infarction and congestive heart failure, and approximately 90% die within the 1st year of life. Rarely,
ALCAPA syndrome manifests in adults; it may be an important cause of sudden cardiac death.
The right coronary artery may be unusually dilated and tortuous with evidence of collateral formation.
Intercoronary collateral arteries along the external surface of the heart or within the interventricular septum may also be seen.
– Due to low pressure of pulmonary artery, blood flows
Right coronary artery → collaterals → left coronary artery → left pulmonary artery
Dilatated tortous appearance of both RCA and LCA.
Reference)
RadioGraphics Vol. 29, No. 2, https://doi.org/10.1148/rg.292085059
