Rare vascular anomaly causing dilatation of azygos vein
Over 80% of patients are related with left isomerism
Hepatic veins are directly drain into right atrium
![](https://q-radiology.com/wp-content/uploads/2022/12/image-29.png)
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CT) Absent hepatic segment of IVC, dilatation of azygos vein
Rare vascular anomaly causing dilatation of azygos vein
Over 80% of patients are related with left isomerism
Hepatic veins are directly drain into right atrium