- The most common cause of abdominal mass in newborns and the most common cystic malformation of the kidney in infancy
- A severe form of nonhereditary dysplasia, which is mostly due to pelvoinfundibular atresia during renal development
- Multiple noncommunicating renal cysts with an intervening echogenic dysplastic parenchyma
- No functioning renal parenchyma and no central renal pelvis in the affected kidney
- Radionuclide imaging(DMSA renal scintigraphy) might be used to further differentiate the hydronephrotic form of MCDK from an obstruction in a functioning kidney
- Mostly unilateral but may be bilateral(fatal) or segmental.
( a ) Longitudinal US of the right kidney shows multiple cysts without normal renal parenchyma.
( b ) An anterior view of DMSA renal scintigraphy shows no uptake of radioisotopes in the right kidney.
( c ) Two years later, most of the cysts have decreased in size and number with the exception of a large cyst in the lower pole
Reference)
Radiology Illustrated: Pediatric Radiology, Springer; 2014th edition
